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產品詳情
  • 產品名稱:Anti-ALG11抗體

  • 產品型號:天門冬酰胺連接糖基化11抗體
  • 產品廠商:KALANG
  • 產品文檔:
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簡單介紹:
Anti-ALG11抗體產品質量穩定,實驗效果明顯,貨期快,價格優惠,歡迎垂詢訂購!我公司長期供應**組化抗體、WB抗體、**組化試劑盒和抗體試驗所需全部相關試劑、熒光標記抗體、單克隆抗體、多克隆抗體、各種標記的二抗IgG/IgM/IgD/IgA等科研實驗抗體。Anti-ALG11抗體用于**組化實驗,WB實驗,相應的標記抗體有HRP標記抗體,FITC標記,BIO等。
詳情介紹:
Rabbit  Anti-ALG11
Cat. Number:
Anti-ALG11抗體KL-7957R
Quantity size:
0.2ml
Concentration:
1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
MannosyltransferaseAnti-ALG11抗體 involved in the last steps of the synthesis of Man5GlcNAc(2)-PP-dolichol core oligosaccharide on the cytoplasmic face of the endoplasmic reticulum. Catalyzes the addition of the 4th and 5th mannose residues to the dolichol-linked oligosaccharide chain.
Involvement in disease:Defects in ALG11 are the cause of congenital disorder of glycosylation type 1P (CDG1P). A multisystem disorder caused by a defect in glycoprotein biosynthesis and characterized by under-glycosylated serum glycoproteins. Congenital disorders of glycosylation result in a wide variety of Anti-ALG11抗體clinical features, such as defects in the nervous system development, psychomotor retardation, dysmorphic features, hypotonia, coagulation disorders, and immunodeficiency. The broad spectrum of features reflects the critical role of N-glycoproteins during embryonic development, differentiation, and maintenance of cell functions.
Also known as:
Asparagine-linked Anti-ALG11抗體glycosylation protein 11 homolog; AI849156; alg11; ALG11_HUMAN; Asparagine-linked glycosylation 11; Asparagine-linked glycosylation 11, alpha-1,2-mannosyltransferase homolog (yeast); GT8; UTP14C.
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.
Reacts with: Human, Mouse, Rat, Dog, Horse, .
Immunogen: KLH conjugated synthetic peptide derived from human ALG11.
Predicted Molecular Weight: 56kDa.
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500 Anti-ALG11抗體 ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.
kl089Hu01 谷胱甘肽S轉移酶κ1(GSTκ1)多克隆抗體 Polyclonal Antibody to Glutathione S Transferase Kappa 1 (GSTk1)
kl090Hu01 谷胱甘肽S轉移酶π1(GSTπ1)多克隆抗體 Polyclonal Antibody to Glutathione S Transferase Pi (GSTp)
kl090Po01 谷胱甘肽S轉移酶π1(GSTπ1)多克隆抗體 Polyclonal Antibody to Glutathione S Transferase Pi (GSTp)
kl091Hu01 肝腎骨堿性磷酸酶(ALPL)多克隆抗體 Polyclonal Antibody to Alkaline Phosphatase, Liver/Bone/Kidney (ALPL)
kl091Mu01 肝腎骨堿性磷酸酶(ALPL)多克隆抗體 Polyclonal Antibody to Alkaline Phosphatase, Liver/Bone/Kidney (ALPL)
kl091Ra01 肝腎骨堿性磷酸酶(ALPL)多克隆抗體 Polyclonal Antibody to Alkaline Phosphatase, Liver/Bone/Kidney (ALPL)
kl092Hu01 骨涎蛋白(BSP)多克隆抗體 Polyclonal Antibody to Bone Sialoprotein (BSP)
kl094Hu01 凝血因子ⅩⅢA1肽(F13A1)多克隆抗體 Polyclonal Antibody to Coagulation Factor XIII A1 Polypeptide (F13A1)
kl097Hu01 運動因子相關蛋白1(MRP1)多克隆抗體 Polyclonal Antibody to Motility Related Protein (MRP1)
kl099Hu01 CD8a分子(CD8a)多克隆抗體 Polyclonal Antibody to Cluster Of Differentiation 8a (CD8a)
kl100Hu01 封閉蛋白18(CLDN18)多克隆抗體 Polyclonal Antibody to Claudin 18 (CLDN18)
kl100Ra01 封閉蛋白18(CLDN18)多克隆抗體 Polyclonal Antibody to Claudin 18 (CLDN18)
kl102Hu01 肌球蛋白輕鏈2(MYL2)多克隆抗體 Polyclonal Antibody to Myosin Light Chain 2, Regulatory, Cardiac (MYL2)
kl105Hu01 肌球蛋白輕鏈1(MYL1)多克隆抗體 Polyclonal Antibody to Myosin Light Chain 1, Alkali, Fast Skeletal (MYL1)

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