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產(chǎn)品詳情
  • 產(chǎn)品名稱:Anti-ALAD抗體

  • 產(chǎn)品型號(hào):δ氨基乙酰丙酸脫水酶抗體
  • 產(chǎn)品廠商:KALANG
  • 產(chǎn)品文檔:
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Anti-ALAD抗體產(chǎn)品質(zhì)量穩(wěn)定,實(shí)驗(yàn)效果明顯,貨期快,價(jià)格優(yōu)惠,歡迎垂詢訂購!我公司長(zhǎng)期供應(yīng)**組化抗體、WB抗體、**組化試劑盒和抗體試驗(yàn)所需全部相關(guān)試劑、熒光標(biāo)記抗體、單克隆抗體、多克隆抗體、各種標(biāo)記的二抗IgG/IgM/IgD/IgA等科研實(shí)驗(yàn)抗體。Anti-ALAD抗體用于**組化實(shí)驗(yàn),WB實(shí)驗(yàn),相應(yīng)的標(biāo)記抗體有HRP標(biāo)記抗體,FITC標(biāo)記,BIO等。
詳情介紹:
Rabbit  Anti-ALAD
Cat. Number:
Anti-ALAD抗體KL-7954R
Quantity size:
0.2ml
Concentration:
1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
Catalyzes an early Anti-ALAD抗體step in the biosynthesis of tetrapyrroles. Binds two molecules of 5-aminolevulinate per subunit, each at a distinct site, and catalyzes their condensation to form porphobilinogen. Involvement in disease:Defects in ALAD are the cause of acute hepatic porphyria (AHP). AHP is a form of porphyria. Porphyrias are inherited defects in the biosynthesis of heme, resulting in the accumulation and increased excretion of porphyrins or porphyrin precursors. They are classified as erythropoietic or hepatic, depending on whether the enzyme deficiency occurs in red blood cells or in the liver. AHP is characterized by attacks of gastrointestinal disturbances, abdominal colic, paralysis, and peripheral neuropathy. Most attacks are precipitated by drugs, alcohol, caloric deprivation, infections, Anti-ALAD抗體or endocrine factors.
Also known as:
ALAD; ALADH; ALADR; Anti-ALAD抗體Aminolevulinate dehydratase; Aminolevulinate, delta, dehydratase; Delta aminolevulinic acid dehydratase; Delta-aminolevulinic acid dehydratase; HEM2_HUMAN; Lv; PBGS; Porphobilinogen synthase.
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.
Reacts with: Human, Mouse, Rat, Dog, Cow, Horse, Rabbit, Sheep, .
Immunogen: KLH conjugated synthetic peptide derived from human ALAD.
Predicted Molecular Weight: 36kDa.
Storage:
Shipped at 4℃, Store Anti-ALAD抗體at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.
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kl054Hu01 凋亡蛋白酶激活因子1(Akl1)多克隆抗體 Polyclonal Antibody to Apoptotic Peptidase Activating Factor 1 (Akl1)
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kl059Hu01 巖藻糖基轉(zhuǎn)移酶4(FUT4)多克隆抗體 Polyclonal Antibody to Fucosyltransferase 4 (FUT4)
kl061Hu01 蛋白二硫鍵異構(gòu)酶(PDI)多克隆抗體 Polyclonal Antibody to Protein Disulfide Isomerase (PDI)
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kl063Hu01 泛素結(jié)合酶E2A(UBE2A)多克隆抗體 Polyclonal Antibody to Ubiquitin Conjugating Enzyme E2A (UBE2A)
kl063Mu01 泛素結(jié)合酶E2A(UBE2A)多克隆抗體 Polyclonal Antibody to Ubiquitin Conjugating Enzyme E2A (UBE2A)
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kl067Mu01 YY肽(PYY)多克隆抗體 Polyclonal Antibody to Peptide YY (PYY)

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