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產(chǎn)品詳情
  • 產(chǎn)品名稱:Anti-ATX2抗體

  • 產(chǎn)品型號:脊髓小腦共濟(jì)失調(diào)2型蛋白抗體
  • 產(chǎn)品廠商:KALANG
  • 產(chǎn)品文檔:
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簡單介紹:
Anti-ATX2抗體產(chǎn)品質(zhì)量穩(wěn)定,實驗效果明顯,貨期快,價格優(yōu)惠,歡迎垂詢訂購!我公司長期供應(yīng)**組化抗體、WB抗體、**組化試劑盒和抗體試驗所需全部相關(guān)試劑、熒光標(biāo)記抗體、單克隆抗體、多克隆抗體、各種標(biāo)記的二抗IgG/IgM/IgD/IgA等科研實驗抗體。Anti-ATX2抗體用于**組化實驗,WB實驗,相應(yīng)的標(biāo)記抗體有HRP標(biāo)記抗體,FITC標(biāo)記,BIO等。
詳情介紹:
Rabbit  Anti-ATX2
Cat. Number:
Anti-ATX2抗體KL-7974R
Quantity size:
0.2ml
Concentration:
1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
The autosomal Anti-ATX2抗體dominant cerebellar ataxias (ADCA) are a heterogeneous group of neurodegenerative disorders characterized by progressive degeneration of the cerebellum, brain stem and spinal cord. Clinically, ADCA has been divided into three groups: ADCA types I-III. ATX2 belongs to the autosomal dominant cerebellar ataxias type I (ADCA I) which are characterized by cerebellar ataxia in combination with additional clinical features like optic atrophy, ophthalmoplegia, bulbar and extrapyramidal signs, peripheral neuropathy and dementia. ATX2 is caused by expansion of a CAG repeat in Anti-ATX2抗體the coding region of ATX2. Longer expansions result in earlier onset of the disease. There are four named isoforms.
Also known as:
Ataxin 2; ATXN2;Anti-ATX2抗體 Olivopontocerebellar ataxia 2, autosomal dominant; SCA2; Spinocerebellar ataxia type 2 protein; TNRC13; Trinucleotide repeat containing gene 13 protein; SRRT_HUMAN.
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.
Reacts with: Human, Mouse, Rat, Chicken, Dog, Pig, Cow, Horse, .
Immunogen: KLH conjugated synthetic peptide derived from human ATX2 (771-815aa).
Predicted Molecular Weight: 101kDa.
Storage:
Shipped at 4℃, Anti-ATX2抗體Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.
kl404Mu01 Thy1細(xì)胞表面抗原(Thy1)多克隆抗體 Polyclonal Antibody to Thy1 Cell Surface Antigen (Thy1)
kl404Ra01 Thy1細(xì)胞表面抗原(Thy1)多克隆抗體 Polyclonal Antibody to Thy1 Cell Surface Antigen (Thy1)
kl406Bo01 脂多糖結(jié)合蛋白(LBP)多克隆抗體 Polyclonal Antibody to Lipopolysaccharide Binding Protein (LBP)
kl406Hu01 脂多糖結(jié)合蛋白(LBP)多克隆抗體 Polyclonal Antibody to Lipopolysaccharide Binding Protein (LBP)
kl406Mu01 脂多糖結(jié)合蛋白(LBP)多克隆抗體 Polyclonal Antibody to Lipopolysaccharide Binding Protein (LBP)
kl406Ra01 脂多糖結(jié)合蛋白(LBP)多克隆抗體 Polyclonal Antibody to Lipopolysaccharide Binding Protein (LBP)
kl416Hu01 葡萄糖苷酸酶β(GUSβ)多克隆抗體 Polyclonal Antibody to Glucuronidase Beta (GUSb)
kl416Mu01 葡萄糖苷酸酶β(GUSβ)多克隆抗體 Polyclonal Antibody to Glucuronidase Beta (GUSb)
kl416Ra01 葡萄糖苷酸酶β(GUSβ)多克隆抗體 Polyclonal Antibody to Glucuronidase Beta (GUSb)
kl426Hu01 CD99分子(CD99)多克隆抗體 Polyclonal Antibody to Cluster Of Differentiation 99 (CD99)
kl429Hu01 多巴胺β羥化酶(DβH)多克隆抗體 Polyclonal Antibody to Dokline Beta Hydroxylase (DbH)
kl430Hu01 信號素4D(SEMA4D)多克隆抗體 Polyclonal Antibody to Semaphorin 4D (SEMA4D)
kl434Hu01 蛋白酶3(PR3)多克隆抗體 Polyclonal Antibody to Proteinase 3 (PR3)
kl434Mu01 蛋白酶3(PR3)多克隆抗體 Polyclonal Antibody to Proteinase 3 (PR3)
kl434Ra01 蛋白酶3(PR3)多克隆抗體 Polyclonal Antibody to Proteinase 3 (PR3)
kl438Hu01 酪氨酸羥化酶(TH)多克隆抗體 Polyclonal Antibody to Tyrosine Hydroxylase (TH)
kl438Mu01 酪氨酸羥化酶(TH)多克隆抗體 Polyclonal Antibody to Tyrosine Hydroxylase (TH)
kl438Ra01 酪氨酸羥化酶(TH)多克隆抗體 Polyclonal Antibody to Tyrosine Hydroxylase (TH)
kl440Hu01 整合素β4(ITGβ4)多克隆抗體 Polyclonal Antibody to Integrin Beta 4 (ITGb4)
kl443Hu01 胎盤蛋白13(PP13)多克隆抗體 Polyclonal Antibody to Placental Protein 13 (PP13)
kl447Ra01 乙酰膽堿酯酶(AchE)多克隆抗體 Polyclonal Antibody to Acetylcholinesterase (AchE)

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