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產品詳情
  • 產品名稱:Anti-ANT-1抗體

  • 產品型號:腺嘌呤核苷酸轉運蛋白1
  • 產品廠商:KALANG
  • 產品文檔:
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簡單介紹:
Anti-ANT-1抗體產品質量穩定,實驗效果明顯,貨期快,價格優惠,歡迎垂詢訂購!我公司長期供應**組化抗體、WB抗體、**組化試劑盒和抗體試驗所需全部相關試劑、熒光標記抗體、單克隆抗體、多克隆抗體、各種標記的二抗IgG/IgM/IgD/IgA等科研實驗抗體。Anti-ANT-1抗體用于**組化實驗,WB實驗,相應的標記抗體有HRP標記抗體,FITC標記,BIO等。
詳情介紹:
Rabbit  Anti-ANT-1
Cat. Number:
Anti-ANT-1抗體KL-6794R
Quantity size:
0.2ml
Concentration:
1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
Defects in SLC25A4 are a cause of progressive external ophthalmoplegia with mitochondrial DNA deletions autosomal Anti-ANT-1抗體dominant type 2 (PEOA2) [MIM:609283]. Progressive external ophthalmoplegia is characterized by progressive weakness of ocular muscles and levator muscle of the upper eyelid. In a minority of cases, it is associated with skeletal myopathy, which predominantly involves axial or proximal muscles and which causes abnormal fatigability and even permanent muscle weakness. Ragged-red fibers and atrophy are found on muscle biopsy. A large proportion of chronic ophthalmoplegias are associated with other symptoms, leading to a multisystemic pattern of this disease. Additional Anti-ANT-1抗體symptoms are variable, and may include cataracts, hearing loss, sensory axonal neuropathy, ataxia, depression, hypogonadism, and parkinsonism.
Also known as:
heart/skeletal muscle Anti-ANT-1抗體isoform T1; Adenine nucleotide translocator 1 (skeletal muscle); Adenine nucleotide translocator 1; ADP; ADP ATP carrier protein 1; ADP ATP carrier protein heart/skeletal muscle isoform T1; ADP/ATP translocase 1; ADT1_HUMAN; ANT 1; ANT; ANT1; ATP carrier protein 1; ATP carrier protein; MSA02; PEO2; PEO3; SLC25A4; Solute carrier family 25 member 4; T1 antibody.
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.
Reacts with: Human, Mouse, Rat, Dog, Pig, Cow, Rabbit, Sheep, .
Immunogen: KLH conjugated synthetic peptide derived from human ATP carrier protein 1/Adenine Nucleotide Translocase 1.
Predicted MolecularAnti-ANT-1抗體 Weight: 33kDa.
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.
kl269Hu01 磷酯酶Cγ1(PLCγ1)多克隆抗體 Polyclonal Antibody to Phospholikle C Gamma 1 (PLCg1)
kl270Hu01 T-細胞激活連接蛋白(LAT)多克隆抗體 Polyclonal Antibody to Linker For Activation Of T-Cell (LAT)
kl270Mu01 T-細胞激活連接蛋白(LAT)多克隆抗體 Polyclonal Antibody to Linker For Activation Of T-Cell (LAT)
kl270Ra01 T-細胞激活連接蛋白(LAT)多克隆抗體 Polyclonal Antibody to Linker For Activation Of T-Cell (LAT)
kl272Bo01 轉運蛋白1(TNPO1)多克隆抗體 Polyclonal Antibody to Transportin 1 (TNPO1)
kl272Hu01 轉運蛋白1(TNPO1)多克隆抗體 Polyclonal Antibody to Transportin 1 (TNPO1)
kl272Mu01 轉運蛋白1(TNPO1)多克隆抗體 Polyclonal Antibody to Transportin 1 (TNPO1)
kl273Hu01 抑制素結合蛋白(INHBP)多克隆抗體 Polyclonal Antibody to Inhibin Binding Protein (INHBP)
kl273Mu01 抑制素結合蛋白(INHBP)多克隆抗體 Polyclonal Antibody to Inhibin Binding Protein (INHBP)
kl273Ra01 抑制素結合蛋白(INHBP)多克隆抗體 Polyclonal Antibody to Inhibin Binding Protein (INHBP)
kl274Bo01 胰島素樣生長因子結合蛋白6(IGFBP6)多克隆抗體 Polyclonal Antibody to Insulin Like Growth Factor Binding Protein 6 (IGFBP6)
kl274Cp01 胰島素樣生長因子結合蛋白6(IGFBP6)多克隆抗體 Polyclonal Antibody to Insulin Like Growth Factor Binding Protein 6 (IGFBP6)
kl274Eq01 胰島素樣生長因子結合蛋白6(IGFBP6)多克隆抗體 Polyclonal Antibody to Insulin Like Growth Factor Binding Protein 6 (IGFBP6)
kl274Hu01 胰島素樣生長因子結合蛋白6(IGFBP6)多克隆抗體 Polyclonal Antibody to Insulin Like Growth Factor Binding Protein 6 (IGFBP6)
kl274Mu01 胰島素樣生長因子結合蛋白6(IGFBP6)多克隆抗體 Polyclonal Antibody to Insulin Like Growth Factor Binding Protein 6 (IGFBP6)
kl274Po01 胰島素樣生長因子結合蛋白6(IGFBP6)多克隆抗體 Polyclonal Antibody to Insulin Like Growth Factor Binding Protein 6 (IGFBP6)

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