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產(chǎn)品詳情
  • 產(chǎn)品名稱:Anti-ATP7A抗體

  • 產(chǎn)品型號:Anti-ATP7A
  • 產(chǎn)品廠商:KALANG
  • 產(chǎn)品文檔:
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簡單介紹:
Anti-ATP7A抗體產(chǎn)品質(zhì)量穩(wěn)定,實(shí)驗效果明顯,貨期快,價格優(yōu)惠,歡迎垂詢訂購!我公司長期供應(yīng)**組化抗體、WB抗體、**組化試劑盒和抗體試驗所需全部相關(guān)試劑、熒光標(biāo)記抗體、單克隆抗體、多克隆抗體、各種標(biāo)記的二抗IgG/IgM/IgD/IgA等科研實(shí)驗抗體。Anti-ATP7A抗體用于**組化實(shí)驗,WB實(shí)驗,相應(yīng)的標(biāo)記抗體有HRP標(biāo)記抗體,FITC標(biāo)記,BIO等。
詳情介紹:
Rabbit  Anti-ATP7A
Cat. Number:
KL-1572R
Quantity size:
0.2ml
Concentration:
Anti-ATP7A抗體1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
Anti-ATP7A抗體Copper-transporting ATPase 1 is an integral membrane protein cycling constitutively between the trans-golgi network and the plasma membrane. It may supply copper to copper-requiring proteins within the secretory pathway, when localized in the trans-golgi network. Under conditions of elevated extracellular copper, it relocalized to the plasma membrane where it functions in the efflux of copper from cells. Defects in ATP7A are the cause of Menkes syndrome; also known as kinky hair disease, an X-linked recessive disorder.
Also known as:
Anti-ATP7A抗體ATP 7A; ATPase Copper Transporting Alpha Polypeptide; ATPase Cu++ transporting alpha polypeptide (Menkes syndrome); ATPase Cu++ transporting alpha polypeptide; Copper pump 1; Copper transporting ATPase 1; Cu++ transporting P type ATPase; MC 1; MC1; Menkes disease-associated protein; Menkes syndrome; MK; MNK; OHS; ATP7A_HUMAN.
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.
Reacts with: Human, Mouse, Rat, Dog, Cow, Horse, Rabbit, .
Immunogen: KLH conjugated synthetic peptide derived from human ATP7A C-terminus.
Predicted Molecular Weight: 163kDa.
Storage:
Anti-ATP7A抗體Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
Anti-ATP7A抗體WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.kl012Hu01 S100鈣結(jié)合蛋白(S100)多克隆抗體 Polyclonal Antibody to S100 Calcium Binding Protein (S100)
kl012Mu01 S100鈣結(jié)合蛋白(S100)多克隆抗體 Polyclonal Antibody to S100 Calcium Binding Protein (S100)
kl012Ra01 S100鈣結(jié)合蛋白(S100)多克隆抗體 Polyclonal Antibody to S100 Calcium Binding Protein (S100)
kl013Cp01 骨成型蛋白2(BMP2)多克隆抗體 Polyclonal Antibody to Bone Morphogenetic Protein 2 (BMP2)
kl013Ga01 骨成型蛋白2(BMP2)多克隆抗體 Polyclonal Antibody to Bone Morphogenetic Protein 2 (BMP2)
kl013Hu01 骨成型蛋白2(BMP2)多克隆抗體 Polyclonal Antibody to Bone Morphogenetic Protein 2 (BMP2)
kl013Mu01 骨成型蛋白2(BMP2)多克隆抗體 Polyclonal Antibody to Bone Morphogenetic Protein 2 (BMP2)
kl013Po01 骨成型蛋白2(BMP2)多克隆抗體 Polyclonal Antibody to Bone Morphogenetic Protein 2 (BMP2)
kl013Ra01 骨成型蛋白2(BMP2)多克隆抗體 Polyclonal Antibody to Bone Morphogenetic Protein 2 (BMP2)
kl013Rb52 骨成型蛋白2(BMP2)多克隆抗體 Polyclonal Antibody to Bone Morphogenetic Protein 2 (BMP2)
kl014Bo01 骨成型蛋白4(BMP4)多克隆抗體 Polyclonal Antibody to Bone Morphogenetic Protein 4 (BMP4)
kl014Ca01 骨成型蛋白4(BMP4)多克隆抗體 Polyclonal Antibody to Bone Morphogenetic Protein 4 (BMP4)
kl014Cp01 骨成型蛋白4(BMP4)多克隆抗體 Polyclonal Antibody to Bone Morphogenetic Protein 4 (BMP4)
kl014Ga01 骨成型蛋白4(BMP4)多克隆抗體 Polyclonal Antibody to Bone Morphogenetic Protein 4 (BMP4)

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